EXTRAMAMMARY PAGET'S DISEASE: A CASE REPORT
DOI:
https://doi.org/10.56238/arev8n1-130Keywords:
Extramammary Paget's Disease, Perianal Disease, ImmunohistochemistryAbstract
Extramammary Paget's disease is extremely rare; it can be primary or associated with other intra-abdominal neoplasms. The most frequent sites are the vulva and scrotum; perianal presentation has a predilection for the male sex. The treatment of choice is wide resection with clear margins; non-surgical therapies are considered in patients unsuitable for surgery. This case demonstrates the use of multimodal surgical and non-surgical treatment therapy in an elderly patient with comorbidities and prior surgery, highlighting the importance of the multidisciplinary team's decision in complex scenarios. This case will help to support individualized management based on a multidisciplinary approach in cases of rare diseases in complex clinical scenarios.
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References
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